Abstract
The loci for BF, C2, C4A, and C4B are very closely linked to each other so that alleles of these plasma protein markers occur in populations in linkage disequilibrium and are inherited as single genetic units called complotypes. These complotypes are coded by a DNA region of the short arm of chromosome 6 embracing approximately 100 kilobases, which serve as a marker of the major histocompatibility complex. We have studied the complotypes of nine families with known HLA-B/DR crossovers. In seven families, the complotypes were inherited with HLA-DR, including in one family with a double recombination. The haplotype HLA-A28, Cw1, B27, FC3, 20, DR4 of JTr resulted from two recombinations between HLA-A2, Cw1, B27, SC42, DR7 and HLA-A28, Cwx or Cw1, B37, FC3, 20, DR4. In the remaining two families (Ro and Lo) the complotypes were inherited with HLA-B. The haplotype A2, Cw5, Bw44, SC30, DR3 of StLo resulted from paternal recombination between the haplotypes A2, Cw5, Bw44, SC30, DR4 and A24, B8, SC01, DR3, and the haplotype A24, Cw4, Bw35, SC31, DR3 of NaRo resulted from maternal recombination between A24, Cw4, Bw35, SC31, DR4 and A26, Bw41, FC31, DR3. Our data suggest that the complotype region maps closer to HLA-D than to HLA-B.
MeSH Terms
Complement C2/genetics
Complement C4/genetics
Complement C4a
Complement C4b
Complement Factor B/genetics
Genetic Linkage
HLA Antigens/genetics
HLA-B Antigens
HLA-DR Antigens
Histocompatibility Antigens Class II/genetics
Humans
Lactoylglutathione Lyase/genetics
Major Histocompatibility Complex
Pedigree
Recombination, Genetic
Chemicals
Complement C2
Complement C4
HLA Antigens
HLA-B Antigens
HLA-DR Antigens
Histocompatibility Antigens Class II
Complement C4a
Complement C4b
Complement Factor B
Lactoylglutathione Lyase
Authors & Affiliations
9 authors, click to expand affiliations / ORCID
Yunis E J
Awdeh Z
Johnson A
Suciu-Foca N
Robinson M A
Hartzman R
Raum D
Fleischnick E
Alper C A
References (27)
27 references, click to expand
-
An improved procedure for starch-gel electrophoresis: further variations in the serum proteins of normal individuals.
Biochem J. 1959 Mar;71(3):585-7
PMID: 13638269
-
Two HLA-linked loci controlling the fourth component of human complement.
Proc Natl Acad Sci U S A. 1978 Oct;75(10):5165-9
PMID: 368809
-
Recombination within the HLA-D region. Correlation of molecular genotyping with functional data.
J Exp Med. 1984 Jul 1;160(1):222-38
PMID: 6330268
-
Linkage of HL-A and GBG.
Vox Sang. 1974;27(4):382-4
PMID: 4414487
-
Complement loci of the HLA complex. Studies on families with intra-HLA crossovers and haplotype associations.
Hum Immunol. 1981 May;2(3):247-54
PMID: 6455398
-
Inversion in the H-2 complex of t-haplotypes in mice.
Nature. 1983 Nov 24-30;306(5941):380-3
PMID: 6316154
-
Genetic polymorphism of the third component of human complement (C'3).
J Clin Invest. 1968 Sep;47(9):2181-91
PMID: 5675433
-
Report of the Committee on the Genetic Constitution of Chromosome 6.
Cytogenet Cell Genet. 1984;37(1-4):47-70
PMID: 6360564
-
Genetic polymorphism of human plasminogen.
Am J Hum Genet. 1980 Sep;32(5):681-9
PMID: 7424908
-
Serum complement 'supergenes' of the major histocompatibility complex in man (complotypes).
Vox Sang. 1983;45(1):62-7
PMID: 6554026
-
The Pi system-inherited variants of serum alpha 1-antitrypsin.
Prog Med Genet. 1970;7:96-111
PMID: 4911922
-
International system for human gene nomenclature (1979) ISGN (1979).
Cytogenet Cell Genet. 1979;25(1-4):96-116
PMID: 295268
-
Report of the committee on the genetic constitution of chromosome 6. Oslo Conference (1981): Sixth International Workshop on Human Gene Mapping.
Cytogenet Cell Genet. 1982;32(1-4):130-43
PMID: 7140356
-
Genetic control of the eighth component of complement.
J Clin Invest. 1979 Sep;64(3):858-65
PMID: 468996
-
Variants of the group-specific component system as demonstrated by immunofixation electrophoresis. Report of a new variant, Gc Boston (Ge B).
Am J Hum Genet. 1975 Nov;27(6):728-36
PMID: 1239191
-
Evidence for linkage between HL-A histocompatibility genes and those involved in the synthesis of the second component of complement.
J Exp Med. 1974 Oct 1;140(4):1108-11
PMID: 4427089
-
Genetic polymorphism in human glycine-rich beta-glycoprotein.
J Exp Med. 1972 Jan;135(1):68-80
PMID: 4109808
-
A molecular map of the human major histocompatibility complex class III region linking complement genes C4, C2 and factor B.
Nature. 1984 Jan 19-25;307(5948):237-41
PMID: 6559257
-
Inherited structural polymorphism of the fourth component of human complement.
Proc Natl Acad Sci U S A. 1980 Jun;77(6):3576-80
PMID: 6932037
-
Family studies of complement C4 and HLA in man.
Hum Genet. 1981;58(3):260-7
PMID: 6948763
-
Inherited structural polymorphism in human C2: evidence for genetic linkage between C2 and Bf.
J Exp Med. 1976 Oct 1;144(4):1111-5
PMID: 978135
-
Genetic polymorphism of human complement C4 and detection of heterozygotes.
Nature. 1979 Nov 8;282(5735):205-7
PMID: 492334
-
PHOSPHOGLUCOMUTASE POLYMORPHISM IN MAN.
Nature. 1964 Nov 21;204:742-5
PMID: 14235665
-
Polymorphism of red cell glyoxalase I (EI: 4.4.1.5); a new genetic marker in man. Investigation of 169 mother-child combinations.
Humangenetik. 1975;27(2):141-3
PMID: 1150236
-
The location of C2, C4, and BF relative to HLA-B and HLA-D.
Immunogenetics. 1981 Mar 1;12(5-6):473-83
PMID: 7216322
-
Genetics of complement C4. Two homoduplication haplotypes C4S C4S and C4F C4F in a family.
Hum Genet. 1982;61(1):36-8
PMID: 7129423
-
RED CELL ACID PHOSPHATASE VARIANTS: A NEW HUMAN POLYMORPHISM.
Nature. 1963 Sep 7;199:969-71
PMID: 14073798