Cystic fibrosis.

The Journal of clinical investigation ·Vol. 80 ·No. 6 ·1987-12-00 ·Pages 1523-6

Welsh MJ, Fick RB

Abstract

暂无摘要

MeSH Terms

Cystic Fibrosis/physiopathology Humans Pancreas/physiopathology Respiratory System/physiopathology Sweat Glands/physiopathology

Authors & Affiliations

2 authors, click to expand affiliations / ORCID

Welsh M J

Department of Internal Medicine, University of Iowa College of Medicine, Iowa City 52242.

Fick R B

References (31)

31 references, click to expand

Demonstration of serum protein differences in cystic fibrosis by isoelectric focusing in thin-layer polyacrylamide gels.
Clin Chim Acta. 1973 Nov 23;49(1):79-91 PMID: 4764342
Electrolyte transport by airway epithelia.
Physiol Rev. 1987 Oct;67(4):1143-84 PMID: 3317457
Fibroblasts from patients with I-cell disease and pseudo-Hurler polydystrophy are deficient in uridine 5'-diphosphate-N-acetylglucosamine: glycoprotein N-acetylglucosaminylphosphotransferase activity.
J Clin Invest. 1981 May;67(5):1574-9 PMID: 6262380
Improved patch-clamp techniques for high-resolution current recording from cells and cell-free membrane patches.
Pflugers Arch. 1981 Aug;391(2):85-100 PMID: 6270629
Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis.
N Engl J Med. 1981 Dec 17;305(25):1489-95 PMID: 7300874
Chloride impermeability in cystic fibrosis.
Nature. 1983 Feb 3;301(5899):421-2 PMID: 6823316
Higher bioelectric potentials due to decreased chloride absorption in the sweat glands of patients with cystic fibrosis.
N Engl J Med. 1983 May 19;308(20):1185-9 PMID: 6843595
Relative ion permeability of normal and cystic fibrosis nasal epithelium.
J Clin Invest. 1983 May;71(5):1410-7 PMID: 6853720
Abnormal ion permeation through cystic fibrosis respiratory epithelium.
Science. 1983 Sep 9;221(4615):1067-70 PMID: 6308769
The carbohydrate content of IgG from patients with cystic fibrosis.
Pediatr Res. 1983 Dec;17(12):931-5 PMID: 6657324
Defective beta adrenergic response of cystic fibrosis sweat glands in vivo and in vitro.
J Clin Invest. 1984 Jun;73(6):1763-71 PMID: 6327771
Pancreatic fluid secretion and protein hyperconcentration in cystic fibrosis.
N Engl J Med. 1985 Feb 7;312(6):329-34 PMID: 3969086
Persistence of abnormal chloride ion permeability in cystic fibrosis nasal epithelial cells in heterologous culture.
Lancet. 1985 Apr 27;1(8435):954-6 PMID: 2859414
Tissue localization and chromosomal assignment of a serum protein that tracks the cystic fibrosis gene.
Nature. 1985 Jun 6-12;315(6019):513-5 PMID: 2582274
Altered fucosylation of membrane glycoproteins from cystic fibrosis fibroblasts.
Pediatr Res. 1985 Apr;19(4):368-74 PMID: 4000763
Cystic fibrosis decreases the apical membrane chloride permeability of monolayers cultured from cells of tracheal epithelium.
Proc Natl Acad Sci U S A. 1985 Sep;82(18):6167-71 PMID: 3862125
Adrenergic secretory responses of submandibular tissues from control subjects and cystic fibrosis patients.
Clin Chim Acta. 1985 Jun 14;148(3):229-37 PMID: 2412733
Testing for cystic fibrosis.
Nature. 1985 Nov 28-Dec 4;318(6044):309 PMID: 2999607
Culture of human nasal epithelial cells on collagen matrix supports. A comparison of bioelectric properties of normal and cystic fibrosis epithelia.
Am Rev Respir Dis. 1985 Dec;132(6):1281-7 PMID: 4073668
An apical-membrane chloride channel in human tracheal epithelium.
Science. 1986 Jun 27;232(4758):1648-50 PMID: 2424085
Altered regulation of airway epithelial cell chloride channels in cystic fibrosis.
Science. 1986 Aug 1;233(4763):558-60 PMID: 2425436
Chloride and potassium channels in cystic fibrosis airway epithelia.
Nature. 1986 Jul 31-Aug 6;322(6078):467-70 PMID: 2426598
Missing Cl conductance in cystic fibrosis.
Am J Physiol. 1986 Oct;251(4 Pt 1):C649-52 PMID: 2429558
Cystic fibrosis and beta-adrenergic response of airway epithelial cell cultures.
Am J Physiol. 1986 Oct;251(4 Pt 2):R818-22 PMID: 3021002
Na+ transport in cystic fibrosis respiratory epithelia. Abnormal basal rate and response to adenylate cyclase activation.
J Clin Invest. 1986 Nov;78(5):1245-52 PMID: 3771796
Circulating and tissue angiotensin systems.
J Clin Invest. 1987 Jan;79(1):1-6 PMID: 3025255
Abnormal apical cell membrane in cystic fibrosis respiratory epithelium. An in vitro electrophysiologic analysis.
J Clin Invest. 1987 Jan;79(1):80-5 PMID: 3793933
A clue to the basic defect in cystic fibrosis from cloning the CF antigen gene.
Nature. 1987 Apr 9-15;326(6113):614-7 PMID: 3561500
Cystic fibrosis. Classical and reverse genetics.
Nature. 1987 Apr 30-May 6;326(6116):824 PMID: 2883580
Permeability properties of cell membranes and tight junctions of normal and cystic fibrosis sweat ducts.
Pflugers Arch. 1987 May;408(5):505-10 PMID: 3601637
Development of a quantitative immunoassay for the cystic fibrosis gene.
Lancet. 1980 Feb 16;1(8164):330-1 PMID: 6101788

Article Info

Journal

The Journal of clinical investigation

Abbr.

J Clin Invest

ISSN

0021-9738

DOI

10.1172/JCI113237

Published

1987-12-00

Pages

1523-6

Language

English

Region

United States

NLM ID

7802877

PMCID

PMC442419

Subset

External Links

PubMed source DOI: 10.1172/JCI113237 PMC Full Text View journal details

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