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PMID: 304395 Published · ppublish English Comparative Study Journal Article

Methods for the detection of haemophilia carriers: a memorandum.

Bulletin of the World Health Organization ·Vol. 55 ·No. 6 ·1977-00-00 ·Pages 675-702
Abstract

This Memorandum discusses the problems and techniques involved in the detection of carriers of haemophilia A (blood coagulation factor VIII deficiency) and haemophilia B (factor IX deficiency), particularly with a view to its application to genetic counselling. Apart from the personal suffering caused by haemophilia, the proper treatment of haemophiliacs places a great strain on the blood transfusion services, and it is therefore important that potential carriers should have precise information about the consequences of their having children.The Memorandum classifies the types of carrier and describes the laboratory methods used for the assessment of coagulant activity and antigen concentration in blood. Particular emphasis is laid on the establishment of international, national, and laboratory (working) standards for factors VIII and IX and their calibration in international units (IU). This is followed by a detailed account of the statistical analysis of pedigree and laboratory data, which leads to an assessment of the likelihood that a particular person will transmit the haemophilia gene to her children. Finally, the problems and responsibilities involved in genetic counselling are considered.

MeSH Terms
Antigens/analysis Blood Coagulation Tests/methods Factor IX/standards Female Genetic Counseling Genetic Linkage Hemophilia A/diagnosis,genetics Hemophilia B/diagnosis,genetics Humans Immunoassay/methods Male Pedigree Probability Statistics as Topic
Chemicals
Antigens Factor IX
References (18)
18 references, click to expand
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Article Info
Journal
Bulletin of the World Health Organization
Abbr.
Bull World Health Organ
ISSN
0042-9686
Published
1977-00-00
Pages
675-702
Language
English
Region
Switzerland
NLM ID
7507052
PMCID
PMC2366710
Subset
IM
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