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PMID: 9861023 Published · ppublish English Journal Article Research Support, U.S. Gov't, P.H.S.

Modeling stochastic gene expression: implications for haploinsufficiency.

Cook DL, Gerber AN, Tapscott SJ

Abstract

There is increasing recognition that stochastic processes regulate highly predictable patterns of gene expression in developing organisms, but the implications of stochastic gene expression for understanding haploinsufficiency remain largely unexplored. We have used simulations of stochastic gene expression to illustrate that gene copy number and expression deactivation rates are important variables in achieving predictable outcomes. In gene expression systems with non-zero expression deactivation rates, diploid systems had a higher probability of uninterrupted gene expression than haploid systems and were more successful at maintaining gene product above a very low threshold. Systems with relatively rapid expression deactivation rates (unstable gene expression) had more predictable responses to a gradient of inducer than systems with slow or zero expression deactivation rates (stable gene expression), and diploid systems were more predictable than haploid, with or without dosage compensation. We suggest that null mutations of a single allele in a diploid organism could decrease the probability of gene expression and present the hypothesis that some haploinsufficiency syndromes might result from an increased susceptibility to stochastic delays of gene initiation or interruptions of gene expression.

MeSH Terms
Computer Simulation Diploidy Gene Expression Regulation Haplotypes Humans Kinetics Models, Genetic Models, Statistical Mutation Phenotype Software Stochastic Processes Time Factors
Authors & Affiliations
3 authors, click to expand affiliations / ORCID
Cook D L
Department of Physiology and Biophysics, University of Washington, Seattle, WA 98105, USA.
Gerber A N
Tapscott S J
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Article Info
Journal
Proceedings of the National Academy of Sciences of the United States of America
Abbr.
Proc Natl Acad Sci U S A
ISSN
0027-8424
Published
1998-12-22
Pages
15641-6
Language
English
Region
United States
NLM ID
7505876
PMCID
PMC28097
Subset
IM
Grants
NIAMS NIH HHS · R01 AR045203 · United States
NIAMS NIH HHS · AR45203 · United States
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