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PMID: 822246 Published · ppublish English Case Reports Journal Article Research Support, U.S. Gov't, P.H.S.

I-cell disease: activities of lysosomal enzymes toward natural and synthetic substrates.

Life sciences ·Vol. 19 ·No. 3 ·1976-08-01 ·Pages 413-20

Wenger DA, Sattler M, Clark C, Wharton C

Abstract

暂无摘要

MeSH Terms
Acetylglucosaminidase/metabolism Acid Phosphatase/metabolism Fibroblasts/enzymology Galactosidases/metabolism Glucuronidase/metabolism Humans Infant Leukocytes/enzymology Lysosomes/enzymology Male Mannosidases/metabolism Mucopolysaccharidosis I/enzymology,pathology alpha-L-Fucosidase/metabolism
Chemicals
Acid Phosphatase Galactosidases Mannosidases Glucuronidase alpha-L-Fucosidase Acetylglucosaminidase
Authors & Affiliations
4 authors, click to expand affiliations / ORCID
Wenger D A
Sattler M
Clark C
Wharton C
Article Info
Journal
Life sciences
Abbr.
Life Sci
ISSN
0024-3205
Published
1976-08-01
Pages
413-20
Language
English
Region
Netherlands
NLM ID
0375521
Subset
IM
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