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PMID: 7737111 Published · ppublish English Journal Article Research Support, Non-U.S. Gov't

Mice lacking glial fibrillary acidic protein display astrocytes devoid of intermediate filaments but develop and reproduce normally.

The EMBO journal ·Vol. 14 ·No. 8 ·1995-04-18 ·Pages 1590-8

Pekny M, Levéen P, Pekna M, Eliasson C, Berthold CH, Westermark B, Betsholtz C

Abstract

Glial fibrillary acidic protein (GFAP) is the main component of the intermediate filaments in cells of astroglial lineage, including astrocytes in the CNS, nonmyelin forming Schwann cells and enteric glia. To address the function of GFAP in vivo, we have disrupted the GFAP gene in mice via targeted mutation in embryonic stem cells. Mice lacking GFAP developed normally, reached adulthood and reproduced. We did not find any abnormalities in the histological architecture of the CNS, in their behavior, motility, memory, blood-brain barrier function, myenteric plexi histology or intestinal peristaltic movement. Comparisons between GFAP and S-100 immunohistochemical staining patterns in the hippocampus of wild-type and mutant mice suggested a normal abundance of astrocytes in GFAP-negative mice, however, in contrast to wild-types, GFAP-negative astrocytes of the hippocampus and in the white matter of the spinal cord were completely lacking intermediate filaments. This shows that the loss of GFAP intermediate filaments is not compensated for by the up-regulation of other intermediate filament proteins, such as vimentin. The GFAP-negative mice displayed post-traumatic reactive gliosis, which suggests that GFAP up-regulation, a hallmark of reactive gliosis, is not an obligatory requirement for this process.

MeSH Terms
Animals Astrocytes/physiology Base Sequence Blood-Brain Barrier/physiology Brain/ultrastructure Brain Chemistry Female Glial Fibrillary Acidic Protein/deficiency,genetics Gliosis Hippocampus/chemistry,ultrastructure Histocytochemistry Intermediate Filaments/physiology Male Mice Mice, Inbred C57BL Mice, Mutant Strains/embryology,growth & development,psychology Molecular Sequence Data Myenteric Plexus/chemistry,ultrastructure Nerve Tissue/anatomy & histology,chemistry,physiology Psychomotor Performance RNA, Messenger/analysis S100 Proteins/isolation & purification Spinal Cord/chemistry,ultrastructure
Chemicals
Glial Fibrillary Acidic Protein RNA, Messenger S100 Proteins
Authors & Affiliations
7 authors, click to expand affiliations / ORCID
Pekny M
Department of Medical Biochemistry, University of Göteborg, Sweden.
Levéen P
Pekna M
Eliasson C
Berthold C H
Westermark B
Betsholtz C
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Article Info
Journal
The EMBO journal
Abbr.
EMBO J
ISSN
0261-4189
Published
1995-04-18
Pages
1590-8
Language
English
Region
England
NLM ID
8208664
PMCID
PMC398251
Subset
IM
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