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PMID: 736038 Published · ppublish English Journal Article Research Support, U.S. Gov't, P.H.S.

Biochemical differences between mutant propionyl-CoA carboxylases from two complementation groups.

American journal of human genetics ·Vol. 30 ·No. 5 ·1978-09-00 ·Pages 455-64

Wolf B, Hsia YE, Rosenberg LE

Abstract

暂无摘要

MeSH Terms

Aminoisobutyric Acids/pharmacology Avidin/pharmacology Cells, Cultured Coenzyme A/metabolism Female Hot Temperature Humans Kinetics Ligases/deficiency,metabolism Models, Biological Phenotype Potassium/pharmacology Propionates Skin/enzymology

Chemicals

Aminoisobutyric Acids Propionates Avidin Ligases Potassium Coenzyme A

Authors & Affiliations

3 authors, click to expand affiliations / ORCID

Wolf B

Hsia Y E

Rosenberg L E

References (19)

19 references, click to expand

Properties and purification of mitochondrial propionyl carboxylase.
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AVIDIN. 1. THE USE OF (14-C)BIOTIN FOR KINETIC STUDIES AND FOR ASSAY.
Biochem J. 1963 Dec;89:585-91 PMID: 14101979
[On the biochemical function of biotin. II. Purification and mode of action of beta-methyl-crotonyl-carboxylase].
Biochem Z. 1961;335:123-67 PMID: 14467590
Some enzymic properties of mitochondrial propionyl carboxylase.
J Biol Chem. 1962 Jul;237:2140-7 PMID: 13903809
Metabolism of propionic acid in animal tissues. VIII. Crystalline propionyl carboxylase.
J Biol Chem. 1961 Jul;236:1917-23 PMID: 13752080
Further studies on the mechanism of the enzymic carboxylation of propionyl-CoA.
Biochim Biophys Acta. 1961 Apr 1;48:426-7 PMID: 13710705
Metabolism of propionic acid in animal tissues. I. Enzymatic conversion of propionate to succinate.
J Biol Chem. 1957 Dec;229(2):965-79 PMID: 13502357
Protein measurement with the Folin phenol reagent.
J Biol Chem. 1951 Nov;193(1):265-75 PMID: 14907713
Genetic complementation of propionyl-CoA carboxylase deficiency in cultured human fibroblasts.
Am J Hum Genet. 1977 Jul;29(4):378-88 PMID: 195466
The biotin-dependent enzymes.
Adv Enzymol Relat Areas Mol Biol. 1971;35:321-442 PMID: 4150153
Investigations of the structure of 3-methylcrotonyl-CoA carboxylase from Achromobacter.
Eur J Biochem. 1975 Dec 1;60(1):259-66 PMID: 1267
Multiple acyl-coenzyme A carboxylases in Pseudomonas citronellolis.
Biochemistry. 1976 Aug 10;15(16):3465-72 PMID: 8091
Propionic acidemia: diagnosis by enzyme assay in frozen leukocytes.
J Pediatr. 1973 Oct;83(4):625-8 PMID: 4729985
Some properties of propionyl CoA carboxylase partially purified from human liver.
Biochem Med. 1973 Jun;7(3):473-8 PMID: 4715570
The distributions of subunit numbers and subunit sizes of enzymes: a study of the products of 100 human gene loci.
Ann Hum Genet. 1976 May;39(4):383-411 PMID: 782337
Structural properties of pyruvate carboxylases from chicken liver and other sources.
Proc Natl Acad Sci U S A. 1975 Nov;72(11):4308-12 PMID: 1105579
Inherited propionyl-Coa carboxylase deficiency in "ketotic hyperglycinemia".
J Clin Invest. 1971 Jan;50(1):127-30 PMID: 5101292
Activation of pig heart propionyl-CoA carboxylase by potassium ions.
Biochim Biophys Acta. 1968 Apr 24;159(1):167-75 PMID: 5650430
The effect of univalent cations on activities catalyzed by bovine-liver propionyl-CoA carboxylase.
Biochim Biophys Acta. 1967 Jul 11;139(2):487-501 PMID: 6034687

Article Info

Journal

American journal of human genetics

Abbr.

Am J Hum Genet

ISSN

0002-9297

Published

1978-09-00

Pages

455-64

Language

English

Region

United States

NLM ID

0370475

PMCID

PMC1685606

Subset

External Links

PubMed source PMC Full Text View journal details

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Biochemical differences between mutant propionyl-CoA carboxylases from two complementation groups.

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