Myelokathexis: chronic neutropenia with hyperplastic bone marrow and hypersegmented neutrophils in two siblings.

Blut ·Vol. 42 ·No. 3 ·1981-03-00 ·Pages 191-6

Bohinjec J

Abstract

The author describes the clinical and pathological characteristics of a chronic neutropenia in two siblings. The disease was probably inherited as an autosomal recessive trait. The clinical course and the results of the laboratory investigations corresponded to the rare cases of "myelokathexis" reported so far.

MeSH Terms

Adult Agranulocytosis/genetics Bone Marrow/pathology Child Chronic Disease Female Humans Neutropenia/genetics,pathology Neutrophils/pathology

Authors & Affiliations

1 authors, click to expand affiliations / ORCID

Bohinjec J

References (9)

9 references, click to expand

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Human bone marrow colony growth in agar-gel.
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'Myelokathexis'. Neutropenia with marrow hyperplasia.
Am J Dis Child. 1977 Jun;131(6):655-8 PMID: 868817
CHRONIC IDIOPATHIC GRANULOCYTOPENIA.
N Engl J Med. 1964 May 7;270:973-9 PMID: 14122792
Feedback inhibition of the development of macrophage and granulocyte colonies. II. Inhibition by granulocytes.
Proc Natl Acad Sci U S A. 1969 Jan;62(1):81-7 PMID: 5253667
The in vitro colony-forming cell and the response to neutropenia.
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Enhancement of colony-stimulating activity production by lithium.
Blood. 1977 Feb;49(2):263-7 PMID: 299818
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Article Info

Journal

Blut

Abbr.

Blut

ISSN

0006-5242

DOI

10.1007/BF01026389

Published

1981-03-00

Pages

191-6

Language

English

Region

Germany

NLM ID

0173401

Subset

External Links

PubMed source DOI: 10.1007/BF01026389

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Myelokathexis: chronic neutropenia with hyperplastic bone marrow and hypersegmented neutrophils in two siblings.

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