Scleroderma and primary biliary cirrhosis.

British medical journal ·Vol. 3 ·No. 5717 ·1970-08-01 ·Pages 258-9

Murray-Lyon IM, Thompson RP, Ansell ID, Williams R

Abstract

Two cases of scleroderma and primary biliary cirrhosis are described. One had systemic sclerosis with primary biliary cirrhosis of six years' duration at the stage of ductular proliferation. The other had the C.R.S.T. syndrome (calcinosis, Raynaud's phenomenon, sclerodactyly, and telangiectases) with primary biliary cirrhosis at the florid stage. Several similar cases were found in a review of other reports, and it is suggested that the association may be due to a common "autoimmune" process.

MeSH Terms

Bile Ducts, Intrahepatic/pathology Calcinosis/complications Female Humans Liver/pathology Liver Cirrhosis, Biliary/complications,pathology Middle Aged Raynaud Disease/complications Scleroderma, Systemic/complications Telangiectasis/complications

Authors & Affiliations

4 authors, click to expand affiliations / ORCID

Murray-Lyon I M

Thompson R P

Ansell I D

Williams R

References (17)

17 references, click to expand

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Article Info

Journal

British medical journal

Abbr.

Br Med J

ISSN

0007-1447

DOI

10.1136/bmj.3.5717.258

Published

1970-08-01

Pages

258-9

Language

English

Region

England

NLM ID

0372673

PMCID

PMC1701186

Subset

External Links

PubMed source DOI: 10.1136/bmj.3.5717.258 PMC Full Text

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