Abstract
Yeast supersuppressor genes capable of masking the effects of several lysine mutant genes (ly(1-1), ly(9-1), ly(2-1)) were studied with respect to their effects on the respective enzymes (saccharopine dehydrogenase, saccharopine reductase, and alpha-amino-adipic acid reductase). In all strains tested, the supersuppressors functioned by allowing enzyme synthesis not found in the unsuppressed mutant. Studies by optical methods of saccharopine dehydrogenase and saccharopine reductase extracted from suppressed ly(1-1) and ly(9-1) cells, respectively, revealed that the K(m) values for these enzymes were significantly greater than those found in wild type. Saccharopine dehydrogenase from suppressed ly(9-1) cells was found to have K(m) values similar to wild type. These findings are consistent with the inference that a supersuppressor may act by enabling nonsense codons to be read, producing altered enzyme protein. Recent findings that lysine degradation in mammals may involve saccharopine and that the human diseases, hyperlysinemia and saccharopinuria, may be due to metabolic blocks in this route of lysine degradation suggest the ly(1-1) and ly(9-1) yeast mutants as models for the human condition and its possible euphenic treatment.
MeSH Terms
Adipates/metabolism
Amino Acids/metabolism
Carbon Isotopes
Chromatography
Culture Media
Enzymes/metabolism
Genetics, Microbial
Genotype
Kinetics
Lysine/biosynthesis,metabolism
Models, Biological
Mutation
Oxidoreductases/metabolism
Phenotype
Saccharomyces/enzymology,growth & development,metabolism
Spectrophotometry
Suppression, Genetic
Chemicals
Adipates
Amino Acids
Carbon Isotopes
Culture Media
Enzymes
Oxidoreductases
Lysine
Authors & Affiliations
2 authors, click to expand affiliations / ORCID
Fjellstedt T A
Ogur M
References (23)
23 references, click to expand
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