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PMID: 3486890 Published · ppublish English Journal Article Research Support, Non-U.S. Gov't Research Support, U.S. Gov't, P.H.S.

An explanation for minor multimer species in endothelial cell-synthesized von Willebrand factor.

The Journal of clinical investigation ·Vol. 77 ·No. 6 ·1986-06-00 ·Pages 2048-51

Lynch DC, Zimmerman TS, Ling EH, Browning PJ

Abstract

Initial synthesis of von Willebrand factor (vWf) by cultured human endothelial cells proceeds by formation of a dimer of pro-vWf subunits. These subunits are found only within the cell and have an apparent molecular weight of 240,000-260,000, as measured by electrophoresis in sodium dodecyl sulfate-polyacrylamide gels. Posttranslational modifications, including proteolytic cleavage, glycosylation, and sulfation, result in the appearance of two additional vWf subunits. The major one migrates with the subunit of plasma vWf at an apparent molecular weight of 220,000-225,000 and the other migrates more slowly than pro-vWf at an apparent molecular weight of 260,000-275,000. These subunits oligomerize to form a set of vWf multimers, which are subsequently secreted into the culture medium. We isolated individual vWf oligomer species from the agarose gel bands and show that vWf minor, or satellite, species differ from major species in subunit composition.

MeSH Terms
Carbohydrate Metabolism Electrophoresis, Polyacrylamide Gel Endothelium/metabolism Female Humans Macromolecular Substances Molecular Weight Pregnancy Protein Processing, Post-Translational Sulfates/metabolism Umbilical Veins/cytology von Willebrand Factor/biosynthesis
Chemicals
Macromolecular Substances Sulfates von Willebrand Factor
Authors & Affiliations
4 authors, click to expand affiliations / ORCID
Lynch D C
Zimmerman T S
Ling E H
Browning P J
References (16)
16 references, click to expand
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Article Info
Journal
The Journal of clinical investigation
Abbr.
J Clin Invest
ISSN
0021-9738
Published
1986-06-00
Pages
2048-51
Language
English
Region
United States
NLM ID
7802877
PMCID
PMC370567
Subset
IM
Grants
NHLBI NIH HHS · HL-15491 · United States
NHLBI NIH HHS · HL-31311 · United States
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