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PMID: 17676373 Published · ppublish English Case Reports Journal Article

Chronic granulomatous disease associated with atypical Kawasaki disease.

Pediatric cardiology ·Vol. 29 ·No. 1 ·2008-01-00 ·Pages 169-71

Yamazaki-Nakashimada MA, Ramírez-Vargas N, De Rubens-Figueroa J

Abstract

Chronic granulomatous disease (CGD) is an infrequent inherited disorder characterized by recurrent infections and abnormal granuloma formation. Patients with CGD have an exuberant inflammatory response and an increased risk of developing autoimmunity. We present the case of a 1-year-old boy with CGD who developed several of the characteristic clinical features of Kawasaki Disease. His illness responded to intravenous immunoglobulin, aspirin, and corticosteroids.

MeSH Terms
Comorbidity Drug Therapy, Combination Glucocorticoids/therapeutic use Granulomatous Disease, Chronic/drug therapy,epidemiology Humans Immunoglobulins, Intravenous/therapeutic use Immunologic Factors/therapeutic use Infant Male Mucocutaneous Lymph Node Syndrome/drug therapy,epidemiology,etiology Prednisolone/therapeutic use
Chemicals
Glucocorticoids Immunoglobulins, Intravenous Immunologic Factors Prednisolone
Authors & Affiliations
3 authors, click to expand affiliations / ORCID
Yamazaki-Nakashimada M A
Department of Clinical Immunology, Instituto Nacional de Pediatría, Insurgentes Sur 3700-C C.P, 04530, Col. Insurgentes Cuicuilco, Mexico City, Mexico. yzki71@yahoo.com.mx
Ramírez-Vargas N
De Rubens-Figueroa J
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Article Info
Journal
Pediatric cardiology
Abbr.
Pediatr Cardiol
ISSN
0172-0643
DOI
10.1007/s00246-007-9011-4
Email
yzki71@yahoo.com.mx
Published
2008-01-00
Epub
2007-00-04
Pages
169-71
Language
English
Region
United States
NLM ID
8003849
Subset
IM
External Links
PubMed source DOI: 10.1007/s00246-007-9011-4 View journal details
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