Abstract
An orally bioavailable and blood-brain barrier penetrating analog of the kinase inhibitor K252a was able to prevent the typical motor deficits in the tau (P301L) transgenic mouse model (JNPL3) and markedly reduce soluble aggregated hyperphosphorylated tau. However, neurofibrillary tangle counts were not reduced in the successfully treated cohort, suggesting that the main cytotoxic effects of tau are not exerted by neurofibrillary tangles but by lower molecular mass aggregates of tau. Our findings strongly suggest that abnormal tau hyperphosphorylation plays a critical role in the development of tauopathy and suggest a previously undescribed treatment strategy for neurodegenerative diseases involving tau pathology.
MeSH Terms
Animals
Carbazoles/chemistry,pharmacology
Disease Models, Animal
Female
Mice
Mice, Inbred C57BL
Mice, Transgenic
Molecular Structure
Motor Activity/physiology
Motor Skills Disorders/physiopathology,prevention & control
Okadaic Acid/pharmacology
Phosphorylation/drug effects
Physical Conditioning, Animal
Rats
Solubility
Transgenes/genetics
tau Proteins/chemistry,genetics,metabolism
Chemicals
Carbazoles
SRN 003-556
tau Proteins
Okadaic Acid
Authors & Affiliations
16 authors, click to expand affiliations / ORCID
Le Corre Sylvie
Sirenade Pharmaceuticals, Am Klopferspitz 19a, 82152 Martinsried, Germany.
Klafki Hans W
Plesnila Nikolaus
Hübinger Gabriele
Obermeier Axel
Sahagún Heidi
Monse Barbara
Seneci Pierfausto
Lewis Jada
Eriksen Jason
Zehr Cynthia
Yue Mei
McGowan Eileen
Dickson Dennis W
Hutton Michael
Roder Hanno M
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