Abstract
Mutations in MEF2A have been implicated in an autosomal dominant form of coronary artery disease (adCAD1). In this study we sought to determine whether severe mutations in MEF2A might also explain sporadic cases of coronary artery disease (CAD). To do this, we resequenced the coding sequence and splice sites of MEF2A in approximately 300 patients with premature CAD and failed to find causative mutations in the CAD cohort. However, we did identify the 21-bp MEF2A coding sequence deletion originally implicated in adCAD1 in 1 of 300 elderly control subjects without CAD. Further screening of approximately 1,500 additional individuals without CAD revealed 2 more subjects with the MEF2A 21-bp deletion. Genotyping of 19 family members of the 3 probands with the 21-bp deletion in MEF2A revealed that the mutation did not cosegregate with early CAD. These studies support that MEF2A mutations are not a common cause of CAD in white people and argue strongly against a role for the MEF2A 21-bp deletion in autosomal dominant CAD.
MeSH Terms
Adult
Aged
Amino Acid Sequence
Base Sequence
Coronary Artery Disease/genetics,metabolism
DNA Mutational Analysis
DNA-Binding Proteins/genetics,metabolism
Exons
Female
Humans
MADS Domain Proteins
MEF2 Transcription Factors
Male
Middle Aged
Molecular Sequence Data
Mutation
Myogenic Regulatory Factors
Pedigree
Polymorphism, Genetic
Transcription Factors/genetics,metabolism
Whites/genetics
Chemicals
DNA-Binding Proteins
MADS Domain Proteins
MEF2 Transcription Factors
MEF2A protein, human
Myogenic Regulatory Factors
Transcription Factors
Authors & Affiliations
9 authors, click to expand affiliations / ORCID
Weng Li
US Department of Energy, Joint Genome Institute, Walnut Creek, California, USA.
Kavaslar Nihan
Ustaszewska Anna
Doelle Heather
Schackwitz Wendy
Hébert Sybil
Cohen Jonathan C
McPherson Ruth
Pennacchio Len A
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