Neurochemistry of the mucopolysaccharidoses: brain glycosaminoglycans in normals and four types of mucopolysaccharidoses.

Adolescent Adult Brain/metabolism Child Child, Preschool Female Glycosaminoglycans/metabolism,urine Heparitin Sulfate Humans Iduronidase/deficiency Infant Intellectual Disability/complications,metabolism Liver/metabolism Male Molecular Weight Mucopolysaccharidoses/complications,metabolism Mucopolysaccharidosis I/metabolism Mucopolysaccharidosis III/metabolism Organ Specificity Spleen/metabolism Sulfatases/deficiency

Glycosaminoglycans Heparitin Sulfate Sulfatases Iduronidase