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PMID: 12393845 Published · ppublish English Case Reports Journal Article Research Support, Non-U.S. Gov't

Beneficial effects of leptin on obesity, T cell hyporesponsiveness, and neuroendocrine/metabolic dysfunction of human congenital leptin deficiency.

The Journal of clinical investigation ·Vol. 110 ·No. 8 ·2002-10-00 ·Pages 1093-103

Farooqi IS, Matarese G, Lord GM, Keogh JM, Lawrence E, Agwu C, Sanna V, Jebb SA, Perna F, Fontana S, Lechler RI, DePaoli AM, O'Rahilly S

Abstract

The wide range of phenotypic abnormalities seen in the leptin-deficient ob/ob mouse and their reversibility by leptin administration provide compelling evidence for the existence of multiple physiological functions of this hormone in rodents. In contrast, information regarding the roles of this hormone in humans is limited. Three morbidly obese children, who were congenitally deficient in leptin, were treated with daily subcutaneous injections of recombinant human leptin for up to 4 years with sustained, beneficial effects on appetite, fat mass, hyperinsulinemia, and hyperlipidemia. Leptin therapy resulted in a rapid and sustained increase in plasma thyroid hormone levels and, through its age-dependent effects on gonadotropin secretion, facilitated appropriately timed pubertal development. Leptin deficiency was associated with reduced numbers of circulating CD4(+) T cells and impaired T cell proliferation and cytokine release, all of which were reversed by recombinant human leptin administration. The subcutaneous administration of recombinant human leptin has major and sustained beneficial effects on the multiple phenotypic abnormalities associated with congenital human leptin deficiency.

MeSH Terms
Animals Child Child, Preschool Energy Metabolism/drug effects Female Humans Leptin/deficiency,genetics,therapeutic use Lymphocyte Activation/drug effects Mice Neurosecretory Systems/drug effects,physiopathology Obesity/drug therapy,genetics,pathology,physiopathology Phenotype Recombinant Proteins/therapeutic use T-Lymphocytes/drug effects,immunology Weight Loss/drug effects
Chemicals
Leptin Recombinant Proteins
Authors & Affiliations
13 authors, click to expand affiliations / ORCID
Farooqi I Sadaf
University Department of Medicine, Department of Clinical Biochemistry, Addenbrooke's Hospital, Cambridge, United Kingdom. afarooqi@hgmp.mrc.ac.uk
Matarese Giuseppe
Lord Graham M
Keogh Julia M
Lawrence Elizabeth
Agwu Chizo
Sanna Veronica
Jebb Susan A
Perna Francesco
Fontana Silvia
Lechler Robert I
DePaoli Alex M
O'Rahilly Stephen
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Article Info
Journal
The Journal of clinical investigation
Abbr.
J Clin Invest
ISSN
0021-9738
Published
2002-10-00
Pages
1093-103
Language
English
Region
United States
NLM ID
7802877
PMCID
PMC150795
Subset
IM
Grants
Wellcome Trust · 068086 · United Kingdom
Medical Research Council · G108/380 · United Kingdom
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