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PMID: 10739755 Published · ppublish English Journal Article Research Support, U.S. Gov't, P.H.S. Twin Study

Effects of HFE C282Y and H63D polymorphisms and polygenic background on iron stores in a large community sample of twins.

American journal of human genetics ·Vol. 66 ·No. 4 ·2000-04-00 ·Pages 1246-58

Whitfield JB, Cullen LM, Jazwinska EC, Powell LW, Heath AC, Zhu G, Duffy DL, Martin NG

Abstract

The aim of this study was to assess and to compare the role of HFE polymorphisms and other genetic factors in variation in iron stores. Blood samples were obtained from 3,375 adult male and female twins (age range 29-82 years) recruited from the Australian Twin Registry. There were 1,233 complete pairs (562 monozygotic and 571 dizygotic twins). Serum iron, transferrin, transferrin saturation with iron, and ferritin were measured, and the HFE C282Y and H63D genotypes were determined. The frequency of the C282Y allele was.072, and that of the H63D allele was.141. Significant sources of variation in the indices of iron status included age, sex, age-sex interaction, body-mass index, and both the C282Y and H63D genotypes. The iron, transferrin, and saturation values of CC and CY subjects differed significantly, but the ferritin values did not. After correction for age and body-mass index, 23% and 31% of the variance in iron, 66% and 49% of the variance in transferrin, 33% and 47% of the variance in transferrin saturation, and 47% and 47% of the variance in ferritin could be explained by additive genetic factors, for men and women, respectively. HFE C282Y and H63D variation accounted for <5% of the corrected phenotypic variance, except for saturation (12% in women and 5% in men). We conclude that HFE CY and HD heterozygotes differ in iron status from the CC and HH homozygotes and that serum transferrin saturation is more affected than is serum ferritin. There are highly significant effects of other as-yet-unidentified genes on iron stores, in addition to HFE genotype.

MeSH Terms
Adult Age Factors Alleles Amino Acid Substitution/genetics Australia Biological Transport Body Mass Index Environment Ethnicity/genetics Female Ferritins/blood,metabolism Gene Frequency Genetic Variation/genetics Genotype HLA Antigens/genetics Haplotypes/genetics Hemochromatosis Protein Histocompatibility Antigens Class I/genetics Humans Iron/blood,metabolism Male Membrane Proteins Middle Aged Polymorphism, Genetic/genetics Sex Factors Statistics as Topic Transferrin/metabolism
Chemicals
HFE protein, human HLA Antigens Hemochromatosis Protein Histocompatibility Antigens Class I Membrane Proteins Transferrin Ferritins Iron
Authors & Affiliations
8 authors, click to expand affiliations / ORCID
Whitfield J B
Biochemistry Department, Royal Prince Alfred Hospital, Camperdown, NSW 2050, Australia. johnwhit@bioc.rpa.cs.nsw.gov.au
Cullen L M
Jazwinska E C
Powell L W
Heath A C
Zhu G
Duffy D L
Martin N G
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Article Info
Journal
American journal of human genetics
Abbr.
Am J Hum Genet
ISSN
0002-9297
Published
2000-04-00
Epub
2000-00-15
Pages
1246-58
Language
English
Region
United States
NLM ID
0370475
PMCID
PMC1288192
Subset
IM
Grants
NIAAA NIH HHS · P50 AA011998 · United States
NIAAA NIH HHS · R01 AA010249 · United States
NIAAA NIH HHS · AA11998 · United States
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